👤 Christoph Möhle
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Immunomodulation with minocycline rescues retinal degeneration in juvenile neuronal ceroid lipofuscinosis mice highly susceptible to light damage.
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Katharina Dannhausen
,
Christoph Möhle
,
Thomas Langmann
· 2018 · Disease models & mechanisms
· added 2026-04-24
Juvenile neuronal ceroid lipofuscinosis (jNCL) is a rare but fatal inherited lysosomal storage disorder mainly affecting children. The disease is caused by mutations in the
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DOI:
10.1242/dmm.033597
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CLN3
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