Organ-specific autoimmune diseases are believed to result from immune responses generated against self-antigens specific to each organ. However, when such responses target antigens expressed promiscuo Show more
Organ-specific autoimmune diseases are believed to result from immune responses generated against self-antigens specific to each organ. However, when such responses target antigens expressed promiscuously in multiple tissues, then the immune-mediated damage may be wide spread. In this report, we describe a mitochondrial protein, branched chain α-ketoacid dehydrogenase kinase (BCKD We demonstrate that BCKD The disease induced by BCKD Show less